1/4. Complete bony fusion of the mandible to the zygomatic complex and maxillary tuberosity: case report and review.Congenital craniofacial disorders represent approximately 20% of all birth defects. One of these disorders is syngnathia, of which only 24 cases have been reported since 1936. Twenty cases involved fusion of the alveolar processes of the maxilla and mandible. Only four are similar to the presented case, which includes bony fusion of the ascending ramus of the mandible to the zygomatic complex and the posterior part of the maxilla. This case report will present details from the 23rd week of gestation to 8 months of age when the infant underwent the first attempt to free the syngnathia. The literature is discussed and a causative mechanism and new classification are proposed.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
2/4. Complete congenital bony syngnathia in a case of oromandibular limb hypogenesis syndrome.Congenital fusion of the maxilla and mandible (syngnathia) is rare and can present in a wide range of severity from single mucosal bands (synechiae) to complete bony fusion (synostosis). Congenital synostosis of the mandible and maxilla is even less common than synechiae, with only 19 cases reported in the literature. Most of them have presented as an incomplete, unilateral fusion. Only three of the reported cases showed more extensive but still incomplete, intermaxillary bony fusion. We present a case of complete bony fusion of the maxilla and mandible associated with a cleft palate, hypoglossia, micrognathia, unilateral choanal atresia, and limb abnormalities as a feature of oromandibular limb hypogenesis syndrome. Details of operative management are presented.- - - - - - - - - - ranking = 0.5keywords = mandible (Clic here for more details about this article) |
3/4. Congenital maxillomandibular fusion: a case report and review of the literature.Congenital fusion of mandible to maxilla (syngnathia) is rare. Only 25 cases of syngnathia have been reported up to date since the first case was reported in 1936. Of these cases only six have involved fusion of the ascending rami of mandible to the maxilla and zygomatic complex. This report is an additional case of syngnathia involving bilateral bony fusion of mandibular horizontal and ascending rami to zygomatic complex and maxilla in a female neonate. Delay in treatment afforded the opportunity to observe the effects on the growth of the patient as she presented again at the age of 3 years.- - - - - - - - - - ranking = 0.33333333333333keywords = mandible (Clic here for more details about this article) |
4/4. Congenital fusion of the maxilla and mandible.Congenital fusion of the maxilla and mandible (syngnathia) is rare and can present in a wide range of severity from single mucosal bands (synechiae) to complete bony fusion (synostosis). Congenital synostosis of the mandible and maxilla is even less common than synechiae, with only 25 cases reported in the literature. Most of them presented as an incomplete, unilateral fusion. A 4-year-old boy was referred to the authors' emergency unit with asphyxia after vomiting. The authors found the child could not open his mouth. His upper and lower jaws were fused, with only a 2- to 3-mm gap in the anterior part. x-rays and computed tomography scans showed that there was a bony fusion of the ramus of the mandible to the zygomatic complex and the posterior part of the maxilla. In addition, there was significant mandible hypoplasia. After performing an osteotomy (to treat the fusion between the bilateral ramus mandible, maxilla, and zygoma), the authors performed a temporomandibular joint reconstruction using a silicon block. After the completion of these procedures, they observed that the mouth could be opened 32 mm. After 2 years of mandibular lengthening performed with an external distracter, the patient's facial appearance and occlusion became more acceptable. An extremely rare case is described, and the existing literature is reviewed.- - - - - - - - - - ranking = 1.5keywords = mandible (Clic here for more details about this article) |