1/3. Anaesthetic management of a child with fibrodysplasia ossificans progressiva.Fibrodysplasia Ossificans Progressiva (FOP) is a rare inherited disease in which progressive ossification of striated muscles leads to severe disability and respiratory impairment early in life and there are associated characteristic congenital skeletal malformations. Although this condition may prove demanding for the anaesthetist, few reports are available regarding anaesthesia in paediatric patients. We review the clinical features of the disease relevant to anaesthesia and describe the perioperative care of an 18-month-old boy with FOP who underwent endoscopic third-ventriculostomy for hydrocephalus associated with a brainstem mass. We emphasize the importance of an appropriate anaesthetic management of these patients, as inadequate care may lead to exacerbation of the disease with permanent sequelae.- - - - - - - - - - ranking = 1keywords = anaesthesia (Clic here for more details about this article) |
2/3. Fibrodysplasia ossificans progressiva.A 14-yr-old boy with fibrodysplasia ossificans progressiva (FOP) presented for surgery for bilateral division of his ossified masseter muscles. patients with FOP may present problems to the anaesthetist, including difficulties with tracheal intubation, restrictive pulmonary disease and abnormalities of cardiac conduction. With our patient sedated the trachea was intubated using a fibrescope and anaesthesia was induced and maintained with nitrous oxide and enflurane in oxygen. ventilation was controlled throughout surgery and recovery was uneventful.- - - - - - - - - - ranking = 0.5keywords = anaesthesia (Clic here for more details about this article) |
3/3. Anaesthesia in myositis ossificans progressiva. A case report and clinical review.An 18-year-old black youth with myositis ossificans progressiva recently underwent eye surgery. The clinical, laboratory and radiological findings are described. The problems associated with anaesthesia are presented and their management is discussed. The condition is briefly reviewed.- - - - - - - - - - ranking = 0.5keywords = anaesthesia (Clic here for more details about this article) |