1/6. Distraction osteogenesis in silver Russell syndrome to expand the mandible.Distraction osteogenesis is a method commonly used to activate bone regeneration in nonunions and osseous defects and for lengthening procedures of tubular bones. This technique involves the sectioning of a bone and the subsequent deliberate, controlled movement of the opposing sectioned edges to lengthen, widen, or reposition a bone, or all three. In this report, a patient with silver Russell syndrome and severe mandibular hypoplasia was treated by means of distraction osteogenesis of the midsymphysis to widen the mandible in concert with sagittal-ramus osteotomies to lengthen the mandible. This treatment created significantly increased arch length in the mandible, which was necessary to facilitate the patient's orthodontic treatment. We believe this is the first reported case of distraction osteogenesis to widen the mandible with the use of a tooth-borne appliance.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
2/6. The dentofacial features of Sanjad-Sakati syndrome: a case report.Sanjad-Sakati syndrome is an autosomal recessive disorder that was first reported by Sanjad et al. in 1988. It is characterized by congenital hypoparathyroidism, severe growth failure and dysmorphic features. The clinical features include deep set eyes, microcephaly, thin lips, depressed nasal bridge with beaked nose, external ear anomalies and learning difficulties. This report presents the case of a 4-year-old patient who was referred to our dental clinic because of pain in her mouth and poor dental health. Oral findings included micrognathic mandible and maxilla, microdontia, enamel hypoplasia as well as severely decayed teeth. Treatment was carried out under general anaesthesia to extract the most severely affected teeth and restore those which could be conserved. It was concluded that these patients have special dental needs; early diagnosis of the affected children is therefore important in order to commence preventive dental therapy and carry out appropriate dental treatment at the optimum time.- - - - - - - - - - ranking = 0.125keywords = mandible (Clic here for more details about this article) |
3/6. pycnodysostosis. Report of a case and review of the Japanese literature, with emphasis on oral and maxillofacial findings.We report a case of pycnodysostosis and review 54 cases of this syndrome in the Japanese literature, with special emphasis on oral and maxillofacial findings. Common findings were as follows: hypoplasia of maxilla and mandible, hypopneumatization of the maxillary sinuses, loss of mandibular angle, a grooved palate, and malpositioned teeth.- - - - - - - - - - ranking = 0.125keywords = mandible (Clic here for more details about this article) |
4/6. Bilateral osteomyelitis of the mandible in pycnodysostosis. A case report.A dwarf suffering from pycnodysostosis was treated for 2 episodes of chronic osteomyelitis of the mandible occurring at an interval of 6 years. Pycnodysostostis, a variant of osteopetrosis, occurs only in dwarfs and is characterised by increased density of bone which may lead to increased susceptibility to fracture and inflammatory disease.- - - - - - - - - - ranking = 0.625keywords = mandible (Clic here for more details about this article) |
5/6. Radiographic observations of pyknodysostosis. Report of a case.A case of pyknodysostosis in a 32-year-old woman has been reported. The patient presented typical skeletal changes, separated cranial sutures, open fontanelles, partial aplasia of the terminal phalanges of the fingers and toes, and brachyphalanges. The oral findings included lesions resembling periapical cementoma, hypoplasia of the maxilla and mandible, crowding of teeth, and a median raphe.- - - - - - - - - - ranking = 0.125keywords = mandible (Clic here for more details about this article) |
6/6. Anaesthetic management of the Kenny-Caffey syndrome using the laryngeal mask.We report the anaesthetic management of a nine-year-old, 6.8 kg, 75 cm tall female with the Kenny-Caffey syndrome presenting for strabismus surgery. Dysmorphic features in our patient included a hypoplastic mandible. A neonatal (size 1) laryngeal mask was successfully used for management of the airway whilst providing surgical access. The general features of this rare syndrome are presented and the literature reviewed.- - - - - - - - - - ranking = 0.125keywords = mandible (Clic here for more details about this article) |