A flavoprotein enzyme that is responsible for the catabolism of LYSINE; hydroxylysine; and tryptophan. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-coa dehydrogenase.


Symptoms and diagnosis

Symptoms:

    


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