(Huntington Chorea; Juvenile Huntington Disease)
A familial disorder inherited as an autosomal dominant trait and characterized by the onset of progressive chorea
in the fourth or fifth decade of life
. Common initial manifestations include paranoia; poor impulse control; depression
; and delusions
. Eventually intellectual impairment; loss of fine motor control; athetosis
; and diffuse chorea
involving axial and limb musculature develops, leading to a vegetative state within 10-15 years of disease
onset. The juvenile variant has a more fulminant course including seizures
; and chorea
. (From Adams et al., Principles of neurology
, 6th ed, pp1060-4)
juvenile HD, akinetic-rigid, or Westphal variant HD.
of Huntington's disease
Huntington's Disease Society
of Huntington's disease in
with Huntington's disease,
Huntington's Disease (HD)
Diagnosis and therapies
Huntington Township, Huntington County, Indiana, Huntington Center (Columbus), Huntington Harbour, Huntington Beach, California, Huntington's Disease Society of America, Huntington Library, Huntington University Math Competition, Huntington Prep School, Archer Milton Huntington, Cabell Huntington Hospital, Huntington High School (Ohio)
- Reported cases - Summary of cases reported on this disease.
- Related terms - Look for sites, images, videos, news and articles about related terms.
- SearchMedica - Professional Medical Search.
- WHO - World Health Organization.
- PubMed - A service of the National Library of Medicine and National Institutes of Health.
- MEDLINE - Literature from the National Library of Medicine.
- MeSH - Medical Subject Headings.
- DeCS - Health Sciences Descriptors.
Comments on "Huntington Disease"
- If a man has huntington disease what is the probability of his son having the disease and what is the probability of his grandson being a carrier? (+)
Leave a message or picture about "Huntington Disease" or enter the forum