1/7. Self-inflicted orodental injury in a child with leigh disease.leigh disease is an inherited progressive mitochondrial neurodegenerative disease that affects the neurological, respiratory and cardiovascular systems and is associated with retardation of the intellectual and physical development. This report describes the case of a 4-year-old boy with leigh disease who presented with self-inflicted traumatic injury to the teeth, alveolar bone, lips and tongue during repeated episodes of intense orofacial spasms. Conservative management of the injury included repositioning the fractured alveolar bone, splinting the traumatized teeth and planning for a mouthguard. However, after a second incident of severe self-induced injury to the teeth and alveolar bone, extraction of the anterior teeth became inevitable to protect the child from further self-mutilation and to allow healing of the injured tissues.- - - - - - - - - - ranking = 1keywords = extraction (Clic here for more details about this article) |
2/7. Self-mutilation behaviour in lesch-nyhan syndrome.lesch-nyhan syndrome (LNS), first described in 1964 by Lesch and Nyhan, is a rare X-linked genetic disorder involving (near) absence of the enzyme hypoxanthine-guanine phosphoribosyl transferase (HPRT). It occurs in 1:100,000 to 380,000 live births (1, 2). The deficiency of HPRT activity leads to an excessive uric acid production resulting in neurological, renal and musculoskeletal manifestations. death usually occurs in the second or third decade from infection or renal failure. Clinical presentation is characterized by mental retardation, choreoathetosis, spasticity, hyperuricemia and cerebral palsy. A characteristic feature of LNS is the appearance of intractable self-injurious behaviour (SIB), usually in the form of severe lip and finger biting, gouging of eyes, face scratching and head banging requiring extreme management techniques such as the application of restraints and or extraction of teeth at an early age. In this case report a unique approach of SIB in LNS is presented.- - - - - - - - - - ranking = 1keywords = extraction (Clic here for more details about this article) |
3/7. Congenital insensitivity to pain--review and report of a case with dental implications.Pain is a protective mechanism for the body. Absence of pain is a symptom in several disorders, both congenital and acquired. The congenital types are present at birth and affect the number and distribution of types of nerve fibers. At present, 5 types of hereditary sensory and autonomic neuropathies have been identified. The various disorders within this group are classified according to the different patterns of sensory and autonomic dysfunction and peripheral neuropathy and the presence of additional clinical features such as learning disability. However, the field is currently moving away from classification based on clinical presentation toward classification based on underlying genetic abnormality. In the absence of pain, patients are at risk of late presentation with illnesses or injuries, and have an increased incidence of traumatic injury. Self-mutilation is an almost invariable feature of these disorders. We report the case of a patient with congenital insensitivity to pain that presented with self-mutilation injuries to his hands and oral tissues caused by biting. The severe nature of these injuries necessitated serial extraction of his primary teeth soon after eruption, which led to a cessation of the problem. The mutilation has not returned following the eruption of the first of his permanent teeth, suggesting that he has learned not to bite himself, even though to do so causes him no discomfort.- - - - - - - - - - ranking = 1keywords = extraction (Clic here for more details about this article) |
4/7. Congenital insensitivity-to-pain with anhidrosis (CIPA): a case report with 4-year follow-up.Congenital Insensitivity-to-pain with anhidrosis (CIPA) is a rare disorder in which pain perception is absent from birth, despite the fact that all other sensory modalities remain intact or minimally impaired and tendon reflexes are present. The challenge in dentistry is to manage the self-mutilation behavior avoiding serious damages especially to oral structures, hands and fingers. A Brazilian case of CIPA is presented and discussed with clinical documentation of the oral-related problems over a 4-year follow-up. A conservative treatment (mouthguard-like appliance) was proposed with the objective to avoid full mouth extraction.- - - - - - - - - - ranking = 1keywords = extraction (Clic here for more details about this article) |
5/7. A preventive approach to oral self-mutilation in lesch-nyhan syndrome: a case report.lesch-nyhan syndrome is a rare X-linked recessive disorder of purine metabolism, caused by complete absence of the enzyme hypoxanthine-guanine phosphoribosyl transferase. persons affected with this incurable disease are developmentally and physically delayed, and suffer from self-injurious behavior. The most typical feature results in partial or total destruction of perioral tissues. The purpose of this paper was to discuss a case of lesch-nyhan syndrome with self-mutilative behavior and lip injuries, including some suggestions of a preventive approach avoiding the extraction of teeth. A soft mouthguard fabricated to prevent the destruction of perioral soft tissues and combined psychiatric pharmacologic therapy proved to have satisfactory results.- - - - - - - - - - ranking = 1keywords = extraction (Clic here for more details about this article) |
6/7. Multiple autoextractions: oral self-mutilation reviewed.Oral self-mutilation occurs in a variety of clinical settings. The etiology of oral self-mutilation can be divided into organic and functional categories. Organic etiologic factors include metabolic and genetic disorders. Functional self-mutilation is performed knowingly, as a response to certain stimuli, and may or may not serve a cognitive purpose. The occurrence of oral self-mutilation with a functional cause represents a diagnostic challenge to practitioners. In this article, a case of autoextraction of multiple posterior teeth in a psychotic 27-year-old white man is presented. Though a wide range of self-mutilation in a person in a psychotic state is well documented, oral self-mutilation, particularly autoextraction, is rare. Although the case reported is extreme in nature, incidence of oral self-mutilation is not uncommon and should be considered in the differential diagnosis of lesions of unknown cause.- - - - - - - - - - ranking = 6keywords = extraction (Clic here for more details about this article) |
7/7. Self-mutilation by tooth extraction.We have described a schizophrenic patient who mutilated himself by extracting two teeth. We reviewed the existing literature on self-mutilation and the psychoanalytic significance of teeth as body parts.- - - - - - - - - - ranking = 4keywords = extraction (Clic here for more details about this article) |