1/7. A child with Henoch-Schonlein nephritis and selective proteinuria--case report.In this paper, we describe a child with Henoch-Schonlein nephritis presenting with nephrotic syndrome and selective proteinuria. Renal biopsy showed ISKDC Class IIIA nephritis. He responded to steroid treatment and is currently well. The significance of renal involvement in Henoch-Schonlein purpura is discussed.- - - - - - - - - - ranking = 1keywords = nephrotic syndrome (Clic here for more details about this article) |
2/7. Berger disease: Henoch-Schonlein syndrome without the rash.Identical 7-year-old twin boys each had a proved adenovirus infection at the same time. A few days later one developed florid Henoch-Schonlein purpura, severe alimentary tract symptoms, and transient joint symptoms. He had an acute nephritic syndrome, which progressed to nephrotic syndrome and renal insufficiency. biopsy showed severe proliferative glomerulonephritis with crescents and marked deposition of IgA, IgG, C3, and fibrin. The second twin had hematuria and abdominal pain but no rash. biopsy showed mesangial proliferative glomerulonephritis with mesangial deposits of IgA and, to a lesser extent, IgG and C3. The appearance was characteristic of Berger disease, and the subsequent clinical course has been that of symptomless microscopic hematuria and recurrent macroscopic hematuria with normal renal function. Immunologic studies have not revealed why these identical twins responded differently to the same provocation. Perhaps Berger disease may be considered a variant of Henoch-Schonlein nephritis.- - - - - - - - - - ranking = 1keywords = nephrotic syndrome (Clic here for more details about this article) |
3/7. nephrotic syndrome in procainamide induced lupus nephritis.We report a case of the nephrotic syndrome occurring in a patient with procainamide induced LE. It was associated with bilateral pleural effusions, pericarditis, fever, positive LE cell preparation and a high titer of antinuclear antibodies. No anti-dna antibodies were found. Renal biopsy showed mesangial proliferation with few IgM and C3 deposits and interstitial infiltrates; electron microscopy revealed subendothelial deposits. Clinical improvement occured after steroid therapy and there was no recurrence 24 months after withdrawal of prednisone.- - - - - - - - - - ranking = 1keywords = nephrotic syndrome (Clic here for more details about this article) |
4/7. radiation nephritis causing nephrotic syndrome.Clinical symptoms of acute radiation nephritis with nephrotic syndrome developed in a fifty-six-year-old woman after abdominal radiation therapy for an astrocytoma of the spinal cord. The diagnosis of radiation nephritis was confirmed by renal biopsy. To our knowledge, this is the first documented case of radiation nephritis associated with nephrotic syndrome.- - - - - - - - - - ranking = 6keywords = nephrotic syndrome (Clic here for more details about this article) |
5/7. Renal vein thrombosis: occurrence in membranous glomerulonephropathy and lupus nephritis.Renal vein thrombosis developed in 11 of 280 patients having either biopsy-proved membranous glomerulonephropathy or systemic lupus erythematosus with nephritis. All 11 also were found to have nephrotic syndrome. In nine, nephrotic syndrome developed before renal vein thrombosis; the diagnoses of nephrotic syndrome and renal vein thrombosis were made simultaneously in the other two. Ten of the 11 patients also had pulmonary emboli at or near the time of renal vein thrombosis.- - - - - - - - - - ranking = 3keywords = nephrotic syndrome (Clic here for more details about this article) |
6/7. Filarial nephritis: a cause of nephrotic syndrome.A 26-year-old male presented with oedema, massive albuminuria and microscopic haematuria. kidney biopsy revealed enlarged cellular glomeruli infiltrated by polymorphs and eosinophils with focal fibrin deposits along the basement membrane. Microfilariae were seen in the lumen of few glomerular capillaries. antistreptolysin titre was negative. The absence of other aetiological factors and presence of microfilariae within glomeruli suggests that nephrotic syndrome may be due to a filarial nephritis.- - - - - - - - - - ranking = 5keywords = nephrotic syndrome (Clic here for more details about this article) |
7/7. A Chinese adolescent girl with Fechtner-like syndrome.We describe a 15-y-old girl with Fechtner-like syndrome, who is the first Chinese reported to have this rare syndrome. She presented with left homonymous hemianopia and neuroimaging revealed haemorrhage in both parietal and occipital lobes. Peripheral blood smear showed macrothrombocytopenia and intracytoplasmic inclusion bodies inside leucocytes. thrombocytopenia and proteinuria responded to intravenous immunoglobulin and pulsed methylprednisolone. This case illustrates that life-threatening haemorrhage can occur in patients with Fechtner syndrome. Although there was no effective treatment reported in the literature, high dose steroid and immunoglobulin seemed to be useful in our patient. Our patient also had nephritic-nephrotic syndrome with renal insufficiency, which is unusual in adolescent female patients.- - - - - - - - - - ranking = 1keywords = nephrotic syndrome (Clic here for more details about this article) |