A pyridoxal phosphate dependent enzyme that catalyzes the decarboxylation of GLYCINE with the transfer of an aminomethyl group to the LIPOIC ACID moiety of the glycine decarboxylase complex h-protein. Defects in P-protein are the cause of non-ketotic hyperglycinemia. It is one of four subunits of the glycine decarboxylase complex.


Symptoms and diagnosis

Symptoms:

    


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