what's the combined name for tricuspid atresia, pulmonary atresia, and hypoplastic right ventricle?

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What is the name for hypoplastic right ventricle, pulmonary atresia, and tricuspid atresia? not just one or two but all three together. what's that called?
and yes a person with all three can survive, my 3 year old daughter is living proof. she had 3 surgeries starting with 4 days old 6 months old and a month shy of 3 years old. we knew before she was born. however, she has some restrictions..
The last post is incorrect. They were referring to tetralogy of fallot, and that includes 1. VSD, 2. Pulmonary Stenosis, 3. Overriding Aorta, and 4. Right Ventricular Hypertrophy. The conditions you described together are not cumulatively referred to as any congenital defect that I am aware of. They are each a diagnosis on their own, and existing together, I am not under the opinion that a patient could survive without immediate corrective surgery, and even then, with a low probability of survival.   (+ info)

Anyone else here have Tricuspid Atresia?

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I am 21 and have this congenital birth defect. I have never met another person with this defect, and from what I hear there aren't many people that 1. Have this defect and 2. Have the defect that are much older than me due to the fact that the corrective surgery was relatively new when I was born.

I was wondering because I wanted to know what type of restrictions others have overcome. Example; Has anyone with my condition given successful birth? Or joined a swim or track team?
Has anyone living with this condition done what they were told was impossible for them?
Hi!

I'm 41, and I have Tricuspid Atresia also! I had my first Surgery in 1967, it was a Glenn Shunt, done at Johns Hopkins Hospital. I later had a modified Blalock-Taussig, done at the University of Alabama-Birmingham Hospital.

I'm like you ,for the longest time I thought I was one of the few with a Congenital Heart Defect, but there are a lot more of us than you might think. ! in 125 people are born with heart defects, and now just over half of us are adults! I'm a member of the Adult Congenital Heart Association, and I can think of FOUR other people with Tricuspid Atresia who post on our message boards, and that's just off the top of my head!

Drop by, register (it's free!) and get involved with the message boards... it is a lot of fun, and you will learn a lot. And you won't feel like you are out there by yourself anymore!  (+ info)

I have Tricuspid Atresia, can I have a baby?

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I just curious about have a baby. I can't find a site that says anything about a mother having this problem but still wanting a baby. Help me!
I found the first source below to have some encouraging information...it is a medical reference site...I suggest that you give it some attention. Although, certain precautions are indicated, it appears that you should be able to carry a baby to term.  (+ info)

Are you familiar with Tricuspid Atresia?

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My 2 year old son has tricuspid atresia and I just wanted to know like how well is your child developing, what obstacles do you have to go through, and can he/she still play like other children.
My son has already had the first two surgery's and we have the last surgery this winter. He is doing well with his I just wanted to know is there anything else to look out for.
Hi! I have a two year old son also with tricuspid atresia. He is getting ready to have a Fontan surgery in a couple of weeks that I am extremely anxious about.

So far his development has been great - he is happy and able to do everything a normal two year old does. He does get winded when walking up stairs and I know his exercise capacity is not perfect. When checked his oxygen saturations are usually around 84%. I hope the Fontan increases them.

For his future, right now I am so worried about his upcoming surgery. After that, I don't know what to expect for him and that is the hardest part. The doctors have said a Fontan circulation is his best chance for a near normal life, so that is all I can hope for. The other thing I hope for is the rapidly advancing cardiac research and development for more solutions for adults with these kinds of congenital heart defects.

Best of luck of for you and your little guy! When my son was born and in the hospital so much, it seems like many people were telling us they knew of older kids and teenagers with the same defects that were happy and that always gave us so much hope.  (+ info)

What is the liver disorder, biliary atresia?

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This is a condition that occurs at birth. The bile
ducts are either blocked or totally absent.
The sites I list below, that you can click on, state
that it can happen because the bile gets trapped
inside the liver and can cause damage or scarring
of the liver cells, known as Cirrhosis or the bile ducts
may be damaged by the body's immune system in
response to a viral infection acquired at birth.
http://www.cincinnatichildrens.org/svc/alpha/l/liver/diseases/biliary.htm
http://en.wikipedia.org/wiki/Biliary_atresia

I hope this information is of some help to you.
Best wishes  (+ info)

why my 9mos. old baby has to face death? what is the cause of having a biliary atresia?

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my 9mos old baby girl is facing death because of biliary atresia. she wont live after 2yrs old. how and why is it a baby so innocent happen to be in this condition? she needs a 3million pesos liver transplant to live! help us pls. janet antiola 09216390975
There is HOPE! Im SO glad I found this question!
My daughter was diagnosed with Biliary Atresia at the YOUNG age of 10 weeks! She was jaundiced from birth and there was a blood test done to find out she had really bad liver functions, and then after some tests at the children's hospital, it was determined she had biliary atresia.
I dont know where you live, but they should do something called a "KASAI" procedure. http://www.chp.edu/CHP/Kasai+Procedure . they will hook up the liver directly to the small intestine because your baby's biliary tree (comes from liver to intestine) is probably completely damaged. Some children the Kasai works for years, and some it doesnt. Most do end up with a liver transplant.
My daughters Kasai didnt work very long, and after a month it was determined that she needed a liver transplant. She got listed in Chicago, at Childrens Memorial hospital and after a few months of waiting she was transplanted! My mother in law, GRANDMA, donated! We did living donor! There are SO many options here in the U.S. and so many GREAT childrens transplant centers! Pittsburgh, Philadelphia, Chicago, Cincinnatti, Atlanta are just a few of the great ones!

Biliary Atresia is an awful disease, and while she has it it will be a long hard road. There could be many hospital stays and what not. But once you get past it, it does get somewhat easier. The Life after transplant is much easier then the life before it!

My daughter is now 8 months post transplant and she is doing great! Her new liver is working well for her. But she is on a lot of medications daily and will always be on one the rest of her life we are told...if you want to have some inspiration go to www.cota.org. There are PATIENT CAMPAIGNS you can look at. It is peoples storys and what they have been through!
Also COTA is a fundraising organization! That is how you can get help financially through all of this :) Look into it!

GOODLUCK AND GOD BLESS!  (+ info)

2 yr old with pulmonary atresia ans vsd?

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Has anyone had any experience with this with there own child, that would like to share some info. We know its a problem with his heart and we are going to bristol hospital soon, but i would love to gear from people with similar experiences. Thanks
Pulmonary atresia is an extremely rare form of congenital heart disease in which the pulmonary valve does not form properly. The pulmonary valve is a flap-like opening on the right side of the heart that allows blood to move to the lungs.
In pulmonary atresia, a solid sheet of tissue forms where the valve opening should be. Because of this defect, blood from the right side of the heart cannot go to the lungs to pick up oxygen.
A ventricular septal defect is one or more openings in the interventricular septum, producing a shunt between ventricles. Large defects result in a significant left-to-right shunt and produce dyspnea with feeding and poor growth. A loud, harsh, holosystolic murmur at the lower left sternal border is common. Recurrent respiratory infections and heart failure may develop. Diagnosis is by echocardiography. Defects may close spontaneously during infancy or require surgical repair. Endocarditis prophylaxis is recommended.  (+ info)

Is there a syndromee with biliary atresia and fibrosarcoma?

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They appear to be separate syndromes. Hope this helps

Biliary atresia is a rare condition in newborn infants in which the common bile duct between the liver and the small intestine is blocked or absent. If unrecognised, the condition leads to liver failure but not (as one might think) to kernicterus. It has no known cause, and the only effective treatment is by surgery or liver transplantation.


[edit]
Symptoms and diagnosis
Initially, the symptoms are indistinguishable from neonatal jaundice, a common phenomenon. Symptoms are usually evident between two and six weeks after birth. Besides jaundice, other symptoms include pale stools, dark urine, swollen abdomen and large hardened liver. Prolonged jaundice that is resistant to phototherapy and/or exchange transfusions should prompt a search for secondary causes. By this time, liver enzymes are generally measured, and these tend to be grossly deranged, hyperbilirubinaemia is conjugated and therefore does not lead to kernicterus. Ultrasound investigation or other forms of imaging can confirm the diagnosis. Further testing include radioactive scans of the liver and a liver biopsy.

Biliary atresia is a very rare disorder. About one in 15,000 to 20,000 babies in the U.S are affected every year. Biliary atresia seems to affect girls slightly more than boys. Within the same family, it is common for only one child in a pair of twins or only one child within the same family to have it. Asians and African-Americans are affected more frequently than Caucasians. There does not appear to be any link to medications taken during pregnancy.

[edit]
Pathophysiology
There is no known cause of biliary atresia.

As the biliary tract cannot transport bile to the intestine, bile is retained in the liver (known as stasis) and results in cirrhosis of the liver.  (+ info)

my baby has a biliary atresia & she needs a liver transplant to live.where could we get help?it cost 3 M Pesos

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Im janet teacher in phil and a mother of janries 8mos old. She has a biliary atresia and she needs a liver transplant to be able to live. eith our kind of work we cannot provide the needed money for her to be save from death. we are pleading for your help. please help us...janet & aries +639216390975
In New Zealand this is free. I am sad to hear that you need this sort of money to get help for your child. I hope someone will fund this for you.
Best of luck....  (+ info)

why newborn have biliary atresia can develop spider angioma?

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I have a son with biliary atresia and from what I understand they are not 100% sure why some people with liver disease get spider angioma. Lots of normal healthy children get them too. I've read that up to 15% of normal children have sider angiomas. It's very common. Pregnant women get them too so some people think that spider angioma might happen when there is too much estrogen. When the liver is sick it cannot fully detoxify circulating estrogen. Some people with liver disease get multiple spider angiomas. My son had spider angioma when he was little but he is 13 now and does not have them anymore. If you visit www.liverfamilies.net you'll meet lots of parents of children with biliary atresia and discussion of spider angioma.  (+ info)

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