Cases reported "Rare Diseases"

Filter by keywords:



Filtering documents. Please wait...

1/26. Pulmonary alveolar microlithiasis after Varicella zoster infection in a patient presenting with antiphospholipid syndrome and discoid lupus.

    We present a case with diagnosis of pulmonary alveolar microlithiasis that illustrates the appearance of this rare chronic lung disease on conventional chest X-ray, high-resolution CT, and transbronchial lung biopsy. This is the first case reported which developed pulmonary alveolar microlithiasis after Varicella zoster infection in a patient with antiphospholipid antibodies and discoid lupus.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

2/26. Very severe aplastic anemia appearing after thymectomy.

    Aplastic anemia is a rare complication of thymoma and is extremely infrequent after thymectomy. We present a case of a 60-year-old woman with very severe aplastic anemia appearing sixteen months after thymectomy for a thymoma. She underwent thymectomy for a thymoma in April 2000. Preoperative examination revealed no hematologic abnormality. About sixteen months after the operation, she was readmitted because of pancytopenia with cough and fever. bone marrow aspiration revealed a very severe hypoplasia in all the three cell lines with over 80% fatty tissue, and chest CT revealed no recurrence of thymoma. Her aplastic anemia had responded to cyclosporine A and granulocyte-colony stimulating factor (G-CSF).
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

3/26. Castleman disease of the pleura: experience with eight surgically proven cases.

    BACKGROUND: Castleman disease of the pleura is unusual, and we present our experience with eight surgically proven cases. methods: Between 1980 and 2002, 8 patients (7 women and 1 man; age range, 20 to 53 years; mean, 26.5 years) with surgically proven, pleural Castleman disease (six hyaline vascular type, one plasma cell type, and one mixed type) were encountered. Their clinical, imaging, and surgical findings were reviewed. RESULTS: Five patients were asymptomatic, 1 had dyspnea, 1 had cough, and 1 experienced chest discomfort. Chest radiography showed a well-circumscribed interlobar, cardiophrenic, or paraaortic mass in 6 patients, a massive effusion in 1, and a focal diaphragmatic bulge in 1. Six tumors showed varying degrees of contrast enhancement (10 to 95 HU; mean, 46 HU) on computed tomography. Three cases appeared as well-defined, heterogeneously hyperintense pleural masses on magnetic resonance imaging. The masses varied in size from 3 to 10 cm (mean, 5.2 cm). Five masses greater than 5 cm had prominent pleural arterial blood supply and severe adhesions requiring thoracotomy and resection of nearby structures for radical tumor excision. blood loss from patients varied between 100 and 850 mL (mean, 620 mL). No tumor recurrence was noted during follow-up (range, 1 to 16 years; mean, 6.5 years). CONCLUSIONS: Pleural Castleman disease predominately affects young women and manifests as a well-circumscribed mass with a varying degree of contrast enhancement on computed tomography and heterogeneity on magnetic resonance imaging. Tumors greater than 5 cm have profuse pleural blood supplies and severe adhesion necessitating open thoracotomy and resection of neighboring structures. Radical resection can produce a satisfactory outcome.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

4/26. Esophageal tuberculosis.

    Esophageal tuberculosis is a rare clinical entity even in adults. Esophageal tuberculosis, can be either primary or secondary, the former is less common as compared to the latter. The authors present a 14-year-old boy, who presented with vomiting, cough, low-grade fever and anorexia for two months. He had a positive mantoux with history of contact to tuberculosis. Upper GI scopy revealed an irregular ulcer in the mid esophagus and the biopsy was suggestive of tuberculosis. The CT scan of the chest showed consolidation left lower lobe with hilar and mediastinal adenopathy. He responded well to ATT.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

5/26. Intrapulmonary cystic benign teratoma: a case report and review of the literature.

    We describe a 41-year-old woman with a short history of retrosternal chest pain and non-productive cough due to a benign intrapulmonary teratoma originating from the left upper lobe. The clinical, CT features of this rare tumor are presented and the relevant literature is discussed.
- - - - - - - - - -
ranking = 3.559155556783
keywords = chest pain, chest
(Clic here for more details about this article)

6/26. Primary malignant lymphoma arising in the pleura without preceding long-standing pyothorax.

    We report a very rare case of primary malignant lymphoma arising in the pleura with no history of persistent pyothorax. A 72-year-old male was hospitalized with dyspnea on effort and chest CT demonstrated a mass along the right chest wall. Right thoracotomy with complete en bloc resection of the pleural tumor was performed. Immunohistochemical examination of the pleural tumor showed that the histology was marginal zone B-cell malignant lymphoma. We considered that this tumor had originated from the soft tissue in the chest wall based on radiographical and surgical findings. As diagnosis and treatment of pleural malignant lymphoma seems to have been difficult in most cases reported in the literature, it is thought that early active and accurate biopsy with large-bore needles, or, if possible, surgical incision for early diagnosis and aggressive surgery to achieve complete resection combined with radiation therapy and/or chemotherapy would be very important for a good prognosis.
- - - - - - - - - -
ranking = 3
keywords = chest
(Clic here for more details about this article)

7/26. Pseudo-tumor of the lung, a rare clinical presentation of dirofilariasis.

    INTRODUCTION: Pulmonary dirofilariasis is an uncommon entity. Known as a zoonotic disease it can affect humans as a secondary host. A pseudo-tumor of the lung called "coin" lesion is usually detected while performing a chest X-ray for another reason. observation: We present a case of pulmonary dirofilariasis due to Dirofilaria sp. in a 72 year old immunocompetent patient who underwent surgery for suspicion of a neoplasm. DISCUSSION: Human pulmonary dirofilariasis should be evoked in asymptomatic patient from endemic area of canine dirofilariasis presenting with a pseudo tumor of the lung.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

8/26. Behcet disease complicated by diffuse alveolar damage.

    We report an extremely rare case of Behcet disease complicated by diffuse alveolar damage, which was fatal in this patient. It manifested as progressive diffuse ground-glass attenuation in both lungs on chest radiographs and high-resolution CT. Ground-glass attenuation was confirmed histopathologically as diffuse alveolar damage without identified etiology by open lung biopsy.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

9/26. F-18 FDG positron emission tomography in non-Hodgkin lymphoma of the breast.

    The breast is an uncommon site of development of extranodal non-Hodgkin lymphoma (NHL). Both primary and secondary involvement of the breast have been reported. A 36-year-old woman diagnosed with NHL underwent multimodality imaging for staging of the disease. CT of the chest revealed no significant abnormalities. Whole-body FDG PET imaging showed intense FDG uptake in the left breast. Cytologic examination confirmed breast involvement by diffuse large B-cell NHL. Although rare, breast involvement characterized by increased FDG uptake can occur in patients with lymphoma. This case highlights the role of FDG PET in patients with suspected lymphoma in dense breasts that can be missed by CT scan and mammogram.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)

10/26. Metastatic pulmonary calcification in renal failure mimicking pulmonary embolism on lung scan.

    Metastatic pulmonary calcification (MPC) characterized by diffuse calcium deposition in the lungs is known to occur in patients with chronic renal failure. However, MPC with pulmonary artery calcification is uncommon and has only been detected in a few patients with severe disorders. A 48-year-old man with chronic renal failure had cough and progressive dyspnea. ventilation-perfusion (V/Q) lung scans showed multiple large-sized mismatched V/Q defects in the left middle and lower zones of lungs, which was consistent with a high probability of pulmonary embolism (PE). The findings of pulmonary scintigraphy resulted from MPC with pulmonary artery calcification, revealed by simultaneous technetium-99m MDP scintigraphy, low-dose computed tomography, and high-resolution computed tomography (HRCT) of the chest.
- - - - - - - - - -
ranking = 1
keywords = chest
(Clic here for more details about this article)
| Next ->


Leave a message about 'Rare Diseases'


We do not evaluate or guarantee the accuracy of any content in this site. Click here for the full disclaimer.