1/7. pulmonary atresia with ventricular septal defect: report of the oldest known surviving case.The case of a 54-year-old housewife, oldest published survivor with pulmonary atresia and a ventricular septal defect (pseudotruncus arteriosus), is reported. Her remarkably favorable course is likely related to the absence of progressive hemodynamic changes, with moderate pulmonary flow adequate for nearly normal arterial oxygenation yet without increasing pulmonary vascular resistance. This case reemphasizes the relationship of longevity to pulmonary blood flow volume with this defect.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |
2/7. pulmonary artery calcification in recipient twins of twin to twin transfusion syndrome: a report of three cases.Twin to twin transfusion syndrome may rarely complicate monochorionic twin gestation, resulting in discordant size of the twins. Cardiac dysfunction and various types of cardiac defects have been described in the recipient twin of this syndrome. pulmonary artery calcification has been described earlier in one case only. We report three recipients of twin to twin transfusion syndrome with pulmonary artery calcification resulting in obstruction of pulmonary trunk in two of these. One case with progressive severe narrowing was successfully operated at four months of age with patch repair of pulmonary artery. He is doing well three years later. The obstruction is moderate in the other case. Calcification in the wall of pulmonary artery may be secondary to vascular injury sustained as a result of volume overloading of the circulation of the recipient twin.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |
3/7. Stress-induced right ventricular ischemia in recurrent pulmonary outflow stenosis in repaired tetralogy of fallot.Radionuclide uptake by the right ventricle during myocardial perfusion imaging is minimal compared with the left ventricular myocardium and is not given much importance. However, right ventricular hypertrophy from pressure or volume overload may increase right ventricular radiotracer uptake and demonstrate reversible stress-induced perfusion abnormalities in the presence of normal coronary arteries. We report a case of right ventricular ischemia secondary to right ventricular hypertrophy from recurrent right ventricular outflow tract stenosis in a patient with repaired tetralogy of fallot. Advances in the management of congenital heart disease have led to more patients surviving to adulthood. These patients subsequently present to cardiologists in adulthood with sequelae or complications arising from previous surgery undertaken during childhood.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |
4/7. Congenital extracardiac shunts with tetralogy of fallot.Congenital extracardiac shunts in tetralogy of fallot may significantly alter the history and clinical findings and also have significant management implications. An unusual variant of severe tetralogy of fallot in a 54-year-old man enabled long survival with minimal symptoms. The patient had pulmonary valvular and infundibular stenosis, a large ventricular septal defect, an overriding aorta, and large volume systemic-to-pulmonary artery shunting from his right internal mammary and accessory internal mammary arteries to his right pulmonary artery.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |
5/7. Extreme right ventricular hypoplasia after relief of severe pulmonary stenosis. Use of balloon catheter occlusion of atrial septal defect in assessing right ventricular function.A patient is described in whom extreme right ventricular hypoplasia and right-to-left shunting through an atrial septal defect occurred after relief of severe pulmonary stenosis. The ability of the hypoplastic right ventricle to deal with an increased volume load was assessed at cardiac catheterisation by occluding the atrial septal defect with a balloon tipped catheter.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |
6/7. Creation of a one-way interatrial communication in the treatment of critical pulmonary stenosis with intact ventricular septum: a case report.BACKGROUND: In biventricular repair of pulmonary outflow tract obstruction with intact ventricular septum, the right ventricle is loaded with total pulmonary blood flow acutely as the right-to-left shunt is abolished by closure of the atrial septal defect (ASD). methods: We designed a one-way interatrial communication by creation of an atrial septal flap to reduce the excessive volume load of the right ventricle. RESULTS: This procedure was successfully performed in a 3-year-old girl undergoing definitive biventricular repair for critical pulmonary stenosis associated with tricuspid stenosis and a small right ventricle. CONCLUSIONS: We believe that creation of a one-way interatrial communication might be a good alternative to adjustable ASD and/or bidirectional Glenn shunt in biventricular repair of critical pulmonary stenosis or pulmonary atresia with intact ventricular septum.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |
7/7. Partial anomalous pulmonary venous drainage associated with intact atrial septum and pulmonary valve stenosis.Partial anomalous pulmonary venous drainage (PAPVD) with an intact atrial septum is a very rare cardiovascular anomaly. Most PAPVD cases can be detected by echocardiographic scanning of the anomalous pulmonary venous connection. This paper describes an asymptomatic 6-year-old boy who was referred because of a heart murmur. An electrocardiogram and two-dimensional echocardiography revealed right heart volume overload. Mild pulmonary valve stenosis and an intact atrial septum were noted. In addition, color flow mapping demonstrated the right upper pulmonary vein connecting to the superior vena cava. This paper emphasizes that two-dimensional echocardiography in conjunction with color flow mapping is a valuable modality in the detection of anomalous pulmonary venous drainage.- - - - - - - - - - ranking = 1keywords = volume (Clic here for more details about this article) |