1/101. Intraosseous fibrous lesions of the jaws: a manifestation of tuberous sclerosis.Four patients previously diagnosed with tuberous sclerosis are reported with intraosseous fibrous lesions of the jaws. review of the literature revealed comparable pathosis occurring in extragnathic bones and several previous reports of similar lesions within the jaws. Therefore, these intraosseous fibrous proliferations are thought to represent an intraoral manifestation of tuberous sclerosis and not coincidental findings. In all 4 cases, the tumors demonstrated significant collagenization with numerous interspersed plump fibroblasts. Although histopathologically similar, the features of the lesions are not specific and also can be found in desmoplastic fibromas and simple odontogenic fibromas. The definitive diagnosis requires appropriate clinicopathologic correlation.- - - - - - - - - - ranking = 1keywords = jaw (Clic here for more details about this article) |
2/101. Cranio-facial fibrous dysplasia in a 38-year-old African woman: a case history.A 38-year-old woman sought treatment with cranio-facial dysplasia involving the cranium, maxilla and the mandible. Her chief complaint was a mandibular swelling, which had appeared about 2 years previously, had gradually enlarged, and was associated with spontaneous pain. x-ray film examination revealed a ground-glass opacity with blurred demarcation and a 99 Tc medronate bone scan disclosed an increase in tracer uptake in the cranium, maxilla and mandible. The rest of the skeleton was not affected. Histological examination of the lesions revealed solid proliferation of spindle-shaped cells associated with islands of osteid and bone trabecullae with Chinese letter pattern and numerous multinucleated giant cells consistent with fibrous dysplasia. The continued osteoblastic activity of involved bones, coupled with the medical condition of the patient, restricted the management of the patient to largely supportive and palliative care.- - - - - - - - - - ranking = 0.0022945064347325keywords = mandible (Clic here for more details about this article) |
3/101. noma: report of a case resulting in bony ankylosis of the maxilla and mandible.noma, or cancrum oris, has been described as a gangrenous infection of the soft and hard tissues of the oronasal region. Prior to the advent of antibiotics the disease was commonly fatal. Now many survive the acute phase of the disease and present the surgeon with formidable problems of repair. This is a report of a presumed case of noma that resulted in bony ankylosis of the maxilla and mandible. Three-dimensional shaded surface CT reconstruction images were especially useful in demonstrating the architecture of the abnormal bone.- - - - - - - - - - ranking = 0.0057362660868313keywords = mandible (Clic here for more details about this article) |
4/101. erdheim-chester disease of the jaws: literature review and case report.erdheim-chester disease is a rare systemic lipogranulomatous disorder of adults that shares some histopathologic features similar to Langerhans' cell histiocytosis and that results in characteristic radiographic changes in the long bones. Relatively few cases have been reported in the jaws. We present a literature review of jaw cases and the first case report to describe detailed radiographic and pathologic features of jaw involvement, as well as clinical, radiographic, and histopathologic follow-up of the untreated jaw lesions.- - - - - - - - - - ranking = 1.3333333333333keywords = jaw (Clic here for more details about this article) |
5/101. tooth eruption in a patient with craniometaphyseal dysplasia: case report.Craniometaphyseal dysplasia (CMD) is a very rare genetic disorder of bone remodeling caused by osteoclast dysfunction. The clinical and radiographical features of oral findings are presented in a sporadic case of CMD in a child (age 10 years, 7 months). An intraoral examination showed severe malocclusions, including anterior crossbite and deep bite. Furthermore, a radiographic examination showed increased radiopacity of the maxilla and mandibular bones due to hyperostosis and sclerosis of the jaw. There was no root resorption of the canines or molars in the primary dentition, although root formation of the permanent teeth was proceeding. Dental age was calculated to be approximately 1 year, 4 months younger than his chronological age. The eruption speed of the permanent lateral incisors after the gingival emergence was shown to be within normal values, and we discuss whether the canines and premolars in the permanent dentition could erupt or not.- - - - - - - - - - ranking = 0.16666666666667keywords = jaw (Clic here for more details about this article) |
6/101. Gigantiform cementoma: clinicopathologic presentation of 3 cases.Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents as multiquadrant, expansile, mixed radiolucent-opaque lesions that cross the midlines of the jaws. Although cases with a familial pattern are noted in a few publications, sporadic cases have been reported without a family history. The term gigantiform cementoma has been used interchangeably with designations of other fibro-osseous entities, yet its application should be restricted by the criteria defined herein. In this article, we report 3 cases of gigantiform cementoma. Clinical, radiographic, and microscopic features of these lesions are presented, along with criteria to differentiate gigantiform cementoma from other fibro-osseous diseases of the jaws. A possible pathogenetic mechanism and treatment recommendations are discussed.- - - - - - - - - - ranking = 0.5keywords = jaw (Clic here for more details about this article) |
7/101. Langerhans cell granulomatosis: a case report of polyostotic manifestation in the jaw.We report the case of a 43-year-old woman who suffered from a polyostotic form of Langerhans cell granulomatosis (LCG) in the mandible and maxilla. The course of the disease was followed for more than 14 years. The disease's progression finally required subtotal resection of the mandible and reconstruction with a microvascular fibula graft. The literature is reviewed for diagnostic and treatment concepts based on the different stages of LCG.- - - - - - - - - - ranking = 0.6689611731014keywords = jaw, mandible (Clic here for more details about this article) |
8/101. cherubism and its charlatans.cherubism is a rare hereditary condition characterised by progressive cystic proliferation of the mandible and maxilla in childhood, followed by post-pubertal involution of the process and jaw remodelling in adulthood. Its name is derived from the cherubic appearance that results from the jaw hypertrophy. Here, we present the case of a young boy with cherubism, in the context of his pedigree, to illustrate the clinical characteristics and their variable expression. We also seek to distinguish cherubism from central giant cell granuloma and giant cell tumour of the jaws, with which it holds a false synonymity.- - - - - - - - - - ranking = 0.50114725321737keywords = jaw, mandible (Clic here for more details about this article) |
9/101. Neonatal permanent jaw constriction because of oral synechiae and Pierre Robin sequence in a child with van der Woude syndrome.OBJECTIVE: To report a newborn with van der Woude syndrome, Pierre Robin sequence, and oral synechiae. Pierre Robin sequence is a rare manifestation of van der Woude syndrome as are oral synechiae. We speculate that the oral synechiae may be causally related to the development of Pierre Robin sequence in this patient.- - - - - - - - - - ranking = 0.66666666666667keywords = jaw (Clic here for more details about this article) |
10/101. The "turban" nevoid basal cell syndrome. Current management with surgery, chemotherapy and immunotherapy."Turban" nevoid basal cell syndrome is a congenital disease that presents with multiple subepidermal epitheliomas, primarily on the scalp. Other secondary findings may be present such as cysts in the mandible and bifid synostotic rib. A combination of treatments proved beneficial in this disease. Surgical excision was used for treatment of large symptomatic lesions such as painful ulcerating and enlarging tumors. Chemotherapy was used to arrest and cause regression of small and dormant lesions. immunotherapy was used to control the primary disease. Such treatment cured most of the disease and offered a fruitful life to the patient, who is presented to illustrate this multiple disciplinary approach.- - - - - - - - - - ranking = 0.0011472532173663keywords = mandible (Clic here for more details about this article) |
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