1/12. Multiple maxillary and mandibular exostoses associated with multiple dermatofibromas: a case report.exostoses of the maxilla and mandible are nodular protuberances of mature bone that need to be accurately distinguished from other more diagnostically significant lesions, notably exosteal osteomas. Multiple dermatofibromas are rare and may be associated with altered immune function. We report the case of an otherwise healthy 47-year-old woman who was first seen with multiple maxillary and mandibular exostoses associated with multiple dermatofibromas. This association has not been previously reported.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
2/12. Craniofacial and dental manifestations of proteus syndrome: a case report.The proteus syndrome is a rare congenital hamartomatous condition that is characterized by a wide range of malformations, sometimes involving the face. Common manifestations include partial gigantism, congenital lipomas, and plantar hyperplasia. In this report we describe the craniofacial clinicopathological development in a girl with proteus syndrome from age 6 to 20 years. The patient had pronounced hemifacial hypertrophy, exostoses in the left parietal region, and enlargement of the inferior alveolar nerve and mandibular canal in the affected region. The dental development of the affected left mandible and maxilla was characterized by extremely premature development and eruption of the primary and permanent teeth and by pronounced idiopathic root resorptions. The multidisciplinary management of the patient and the treatment outcome is reported. A review of the Proteus patients in the literature who exhibited manifestation in the craniofacial region is presented.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
3/12. Autosomal dominant osteosclerosis.Two cases of a craniotubular hyperostosis are presented. The radiographic features closely resemble Van Buchem disease (hyperostosis corticalis generalisata; endosteal hyperostosis, recessive type), including symmetrical and bilateral diaphyseal cortical thickening of the long and short tubular bones as well as sclerosis and thickening of the calvaria, mandible, shoulder and pelvic girdles, and thoracic cage. Unlike Van Buchem disease, no periosteal excresences are observed, alkaline phosphatase is normal, no basal foramina encroachment of the skull is present, and the genetic pattern is dominant inheritance. These cases possibly represent a separate disorder rather than a variant of Van Buchem disease.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
4/12. Differences between florid osseous dysplasia and chronic diffuse sclerosing osteomyelitis.Florid osseous dysplasia (FOD) is confused in the literature with chronic diffuse sclerosing osteomyelitis. Two cases of each condition are presented to demonstrate the differences between them. In FOD, there are multiple lobulated sclerotic masses in several quadrants of the jaws, usually in black females. In some cases, the sclerotic masses are exposed to the oral cavity, resulting in a secondary osteomyelitis. Periapical cemental dysplasia is often found in association with FOD. Chronic diffuse sclerosing osteomyelitis is a primary inflammatory condition of the mandible. patients have cyclic episodes of unilateral pain and swelling. The affected region of the mandible exhibits a diffuse opacity with poorly defined borders. Although women are affected more often than men, black persons are not particularly susceptible.- - - - - - - - - - ranking = 2.1835931310752keywords = mandible, jaw (Clic here for more details about this article) |
5/12. A unilateral mesenchymal disorder of the head.A hitherto undescribed group of lesions consisting of cystic bony lesions, exostosis, fibromatous lesion, unilateral tonsillar hypertrophy, epidermoid cyst (cholesteatoma) and hyperplasia of the mandible confined to the left side of the face is reported. The case may represent a variant of the proteus syndrome.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
6/12. Osteochondromatous exostosis of the condyle.Osteochondromatous exostosis of the condyle is rare. When these exotoses become large, they can cause temporomandibular pain and clicking with mandibular movements. Treatment consists of surgical removal of the mass. Adjunctive care may include use of intermaxillary fixation, training elastics, and jaw exercises.- - - - - - - - - - ranking = 0.18359313107515keywords = jaw (Clic here for more details about this article) |
7/12. Dental and bone abnormalities in patients with familial polyposis coli.Dental and bone abnormalities of the maxilla and mandible are present in approximately 80% of patients with familial polyposis coli. The dental abnormalities include impacted teeth (other than third molars), supernumerary teeth, congenitally missing teeth, fused roots of first and second molars, and unusually long and tapered roots of posterior teeth. The bone lesions consist mostly of osteomas, either isolated or in clusters, in the maxilla and mandible or of exostoses with lateral and/or lingual extensions. Since dental and bone abnormalities are already present early in life there is a strong suggestion that they may be used as diagnostic features in the recognition of familial polyposis coli.- - - - - - - - - - ranking = 2keywords = mandible (Clic here for more details about this article) |
8/12. The gardner syndrome.The gardner syndrome is characterized by polyposis coli and multiple hard and soft tissue tumors. A case of a 17-year-old male is presented who complained of painless and hard swellings on the angle of the mandible bilateraly. The patient presented the original triad of lesions of the gardner syndrome. On the panoramic X-ray, characteristic radio-opaque lesions (exostoses and enostoses) on the jaws were shown and a compound odontoma was detected in the left side of the mandible.- - - - - - - - - - ranking = 2.1835931310752keywords = mandible, jaw (Clic here for more details about this article) |
9/12. Subpontic osseous proliferation.Nine patients, five women and four men, demonstrated bone growth in an edentulous region of the posterior mandible covered with a pontic. The reasons for this bone growth could include genetic predetermination, functional stresses, and chronic irritation. This bone growth has important clinical and basic science implications. The condition was seen only in adults, only in the mandibular posterior region, and with a variety of pontic designs. Subpontic osseous proliferation was documented in nine patients, but no conclusion about the etiology was made.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
10/12. Familial basal cell nevus syndrome.The basal cell nevus syndrome is characterized by multiple basal cell nevi and basal cell carcinoma, cysts of the jaw, anomalies of ribs and spine, abnormal calcifications, and additional anomalies of the facial skull. A German family is described with manifestations of the syndrome in the mother and her three daughters. Expressivity was variable, in part due to age effects. The observation conforms to the assumed autosomal dominant mode of inheritance with high penetrance.- - - - - - - - - - ranking = 0.18359313107515keywords = jaw (Clic here for more details about this article) |
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