1/10. Combined surgical and orthodontic management of the oral abnormalities in children with cleidocranial dysplasia.Children with cleidocranial dysplasia have dental abnormalities which combine to prevent normal tooth eruption, and which if untreated may result in abnormal facial and jaw growth. A technique combining orthodontics and oral surgery has resulted in the establishment of excellent occlusion and facial appearance in these patients. Recent advances in direct enamel bonding techniques for orthondontic attachments have permitted a conservative surgical approach with minimal bone removal during surgery to expose unerupted teeth prior to orthodontic treatment.- - - - - - - - - - ranking = 1keywords = jaw (Clic here for more details about this article) |
2/10. Pyknodysostosis--a report of two cases with a brief review of the literature.Pyknodysostosis is a rare sclerosing bone disorder that has an autosomal dominant trait. It is characterized by short stature, brachycephaly, short and stubby fingers, open cranial sutures and fontanelle, and diffuse osteosclerosis, where multiple fractures of long bones and osteomyelitis of the jaw are frequent complications. We present a report of two cases of pyknodysostosis with evidence of long bone fractures and chronic suppurative osteomyelitis of the jaws in one of the cases. Some of the specific oral and radiological findings that are consistent with pyknodysostosis are reported, along with a brief review of the literature.- - - - - - - - - - ranking = 2keywords = jaw (Clic here for more details about this article) |
3/10. Histological and analytical studies of a tooth in a patient with cleidocranial dysostosis.A histopathological and analytical study of a permanent tooth from a patient with cleidocranial dysostosis (CCD) was performed. The patient was a 47-year-old woman, who had 10 erupted permanent teeth and 2 partially erupted and 19 completely impacted teeth, including supernumerary teeth. The erupted right upper premolar was extracted and observed using a light microscope and an electron probe X-ray microanalyzer (EPMA). Findings showed enamel hypoplasia, predominantly irregular globular dentin and Tomes' granular layer, and a complete lack of cellular cementum in the ground section. The incremental von Ebner and counter Owen lines were obscure. Comparative quantitative analysis using the EPMA showed that the quantities of calcium and phosphate were lower in the enamel and dentin than those of the control sample.- - - - - - - - - - ranking = 0.01534434940652keywords = lower (Clic here for more details about this article) |
4/10. Treatment of a patient with cleidocranial dysplasia using osseointegrated implants: a patient report.This patient report describes the treatment of a 42-year-old woman with cleidocranial dysplasia. Endosseous implants were used to restore the mandibular and maxillary arches with fixed prostheses. Six implants were placed in the mandible and immediately loaded with an acrylic resin fixed prosthesis. In the maxillary arch, 10 implants were submerged for 4 months prior to functional loading. A transitional denture was relined and placed in the maxilla 10 days after implant placement. Three months later, a definitive mandibular prosthesis was fabricated. The definitive maxillary restoration was delivered 6 months after surgery. The most recent follow-up, 6 months after delivery, confirmed a satisfactory treatment result to date.- - - - - - - - - - ranking = 7.1475521567498keywords = mandible (Clic here for more details about this article) |
5/10. Dental treatment strategies in cleidocranial dysplasia.Based on the findings of our recent longitudinal study on the abnormalities of the dentition in cleidocranial dysplasia (CCD), a hypothesis has been proposed, which makes it possible to predict time of onset of formation of supernumerary teeth and their location in the jaws. It was found that a diagnosis should be made early so that formation of supernumerary teeth can be diagnosed and early intervention undertaken. It should be possible to diagnose supernumerary incisors at about 5-7 years of age and supernumerary canines and premolars a few years later. When root length of the normal permanent teeth has reached about one third of its final length, the overlying supernumerary teeth should be removed, together with overlying bone and primary teeth. In regions where no supernumerary teeth are formed, eruption may also be improved by removal of the primary teeth and surgical exposure of the underlying permanent teeth. Conventional orthodontic treatment and eventually autotransplantation of teeth may still be necessary in the future, but it can be anticipated that the new strategy, with much earlier intervention, will materially reduce the extent of surgical and orthodontic interventions, which have previously been of extremely long duration, tedious to the patients and often of limited success.- - - - - - - - - - ranking = 1keywords = jaw (Clic here for more details about this article) |
6/10. Morphologic characteristics of masseter muscle in cleidocranial dysplasia: a report of 3 cases.cleidocranial dysplasia (CCD) is a rare autosomal dominant skeletal dysplasia. In order to define the morphologic characteristics of the masseter muscle incidental to bone abnormalities, we present 3 cases of CCD with the masseter muscle thickness and maxillofacial bone abnormalities, using computed tomography (CT) and panoramic radiographs. In CCD patients (a) the masseter muscles were less thick than in age- and sex-matched control subjects, (b) the zygomatic arch was discontinuous with the hypoplastic zygomatic bone, (c) the ascending ramus of the mandible had parallel-sided borders, and (d) the coronoid process pointed upwards and/or posteriorly. We have concluded the masseter muscles are less thick than normal, alongside the maxillofacial bone abnormalities in CCD patients.- - - - - - - - - - ranking = 7.1475521567498keywords = mandible (Clic here for more details about this article) |
7/10. cleidocranial dysplasia: diagnostic criteria and combined treatment.cleidocranial dysplasia (CCD) is an uncommon, generalized skeletal disorder characterized by delayed ossification of the skull, aplastic or hypoplastic clavicles, and serious, complex dental abnormalities. There are many difficulties in the early diagnosis of CCD because a majority of the craniofacial abnormalities becomes obvious only during adolescence. In the present case, a hypoplastic midface, a relative prognathia of the mandible, and close approximation of the shoulders in the anterior plane were the conspicuous extraoral findings. Prolonged exfoliation of the primary dentition, unerupted supernumerary teeth, and the irregularly and partially erupted secondary dentition produced occlusional anomalies. The presence of the second permanent molars together with the primary dentition and wide spacing in the lower incisor area were typical dental signs. Gradual extraction of the supernumerary teeth and over-retained primary teeth was the first step of oral surgery. This was followed by a surgical exposure of the unerupted teeth by thinning of the cortical bone. Orthodontic treatment was aimed at parallel growth of the jaws. Removable appliances were used to expand the narrow maxillary and mandibular arches, and a Delaire mask compensated for the lack of sagittal growth of the upper jaw. Temporary functional rehabilitation was solved by partial denture. When the jaws have been fully developed, implant insertions and bridges are the therapeutic measures. The reported case and the literature data support the importance of the early diagnosis and interdisciplinary treatment of CCD.- - - - - - - - - - ranking = 10.162896506156keywords = mandible, jaw, lower (Clic here for more details about this article) |
8/10. Development of the skull in infants with cleidocranial dysplasia.The purpose of the present paper is to clarify some of the questions regarding pathogenesis in cleidocranial dysplasia (CCD) in order to improve the understanding of the mechanisms leading to the craniofacial abnormalities characteristic for young and adult patients with the syndrome. The neonatal skull is described and craniofacial development from birth to 7 years analyzed. skull radiographs of 11 CCD patients ages 0-7 years were examined. Study methods included plain radiographs of the skull and roentgencephalometric films in the lateral, frontal, and axial projections. In one patient, CT scans of the skull with 3-D reconstructions were available. Common to the four patients examined within the first 6 months postnatally was a marked delay of skeletal maturity. In the calvaria a severe reduction of calcification in all bones was found. Corresponding to the expected sutural areas, gaping defects were recorded, indicating that calcification of calvarial bones in the newborn CCD individual had only reached a stage corresponding to around 20 weeks gestational age. Calvarial size corresponded to that of normal newborns and the morphology was relatively normal, taking into account the pronounced deformation that took place during parturition due to the soft, undermineralized skull. At birth bony islands could be observed in the periphery of the occipital, parietal, and frontal bones. Ossification of the maxilla and the mandible seemed to be within normal limits. Posteriorly to the foramen magnum, the chondral part of the supraoccipital bone remained unossified. In the cranial base an increased width of the spheno-occipital synchondrosis was found.(ABSTRACT TRUNCATED AT 250 WORDS)- - - - - - - - - - ranking = 7.1475521567498keywords = mandible (Clic here for more details about this article) |
9/10. Cleidocranial dysostosis: report of a case.This case of cleidocranial dysostosis showed nearly 40 accessory teeth and the unerupted teeth on radiological examinations. Other diagnostic procedures found hypoplasia in maxillary and zygomatic bones, deep palate, open fontanel and open sutures, the collapse of sagittal suture, and aplasia of the clavicle. There were some abnormalities of the fingers. Under general anesthesia eleven supernumerary teeth in the mandible and eight in the maxilla were surgically extracted. Upper and lower removable acrylic appliances were fabricated.- - - - - - - - - - ranking = 7.1628965061563keywords = mandible, lower (Clic here for more details about this article) |
10/10. Morphological changes of the mandible and temporomandibular joints in a patient with cleidocranial dysostosis.The morphology of the dentition and facial parts of the skull in a 17-year-old girl with cleidocranial dysostosis are described. The opening movement of the mandible was limited to 18 mm. Radiological examination demonstrated that this limitation was due to deformities of the temporomandibular joints. To our knowledge, such deformities have not been described in the literature.- - - - - - - - - - ranking = 35.737760783749keywords = mandible (Clic here for more details about this article) |
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