1/20. A newly recognized syndrome of skeletal dysplasia with opalescent and rootless teeth.A Thai girl with skeletal dysplasia and dental anomalies was seen. Her anomalies consisted of disproportionately short stature, short neck, broad and depressed nasal bridge, broad chest in the anteroposterior dimension, kyphosis, widely spaced nipples, and protruded abdomen. Radiographic testing indicated that she had a large sella turcica, platyspondyly, hypoplastic acetabulum, and a small body of mandible. Both her deciduous and permanent teeth were equally opalescent, and most were rootless, with root development of the mandibular teeth more severely affected. Some maxillary roots were extremely short and tapered. Hypodontia was also observed. These findings represent a unique and hitherto undescribed syndrome of skeletal dysplasia with concomitant dental anomalies.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
2/20. temporomandibular joint ankylosis: a case report.This report is based on a case of temporomandibular joint ankylosis discovered in a cadaver during routine student dissection in the Department of anatomy at tokyo Dental College. Extensive osseous ankylosis in the left temporomandibular joint was evident in this case which exhibited a distinctive bird-like facial deformity caused by a mandibular growth disorder. This resulted in the underdevelopment of the mental area in particular. Furthermore, abnormally enlarged antegonal notching was present along the inferior border of the mandible anterior to the angle. Both these manifestations indicated the likelihood that the ankylosis had contributed to the abnormalities and had commenced at an early stage of skeletal development.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
3/20. Clinical manifestations of terminal osseous dysplasia and pigmentary defects in a young girl.Terminal osseous dysplasia and pigmentary defects is a rare X-linked dominant disorder with prenatal male lethality. Affected females display multiple systemic abnormalities such as limb deformities and pigmented lesions of the face and scalp. Phenotypic expression of the syndrome varies among the affected individuals. In this case report, we describe the syndromic dental and oral abnormalities in a female child aged 3 and 1/2 years. A widened bigonial width of the mandible and a brachyfacial pattern are observed. Intraoral findings include multiple frenulae, shallow mucobuccal fold, hypodontia, conical incisors, and other developmental structural defects.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
4/20. Localized osteodysplasia of the mandible in a seven-year-old child: a case report.AIM: This report concerns the most recent knowledge on osteodysplasies, anomalies in the development of the bone tissue, that may concern one or more skeleton segments affecting children. CASE REPORT: The case of a 7-year-old patient is reported, whose left hemimandible showed a radio transparency with a size of 10 x 7 mm. After the usual preliminary diagnostic investigations, it was decided to carry out an ablation. The neoplastic formation was completely enucleated using a conservative operation technique.- - - - - - - - - - ranking = 5keywords = mandible (Clic here for more details about this article) |
5/20. Craniometaphyseal dysplasia associated with obstructive sleep apnoea syndrome.Craniometaphyseal dysplasia (CMD) is a genetic craniotubular bone disorder characterized by early progressive hyperostosis and sclerosis of the craniofacial bones, and abnormal modelling of the metaphyses of the tubular bones. We present the case of a patient with a confirmed history of the autosomal dominant form of CMD, associated with symptoms of obstructive sleep apnoea syndrome. Examination and imaging studies revealed several unusual features in addition to the common findings of CMD such as: bimaxillary retrusion with hyperostosis of the mental area, severe notching of the external occipital protuberance, huge occipital horn, decreased angle of the mandible with notching of the body and thickening of the areas of muscle attachment, and macrodontia. The literature and differential diagnoses are reviewed.- - - - - - - - - - ranking = 1keywords = mandible (Clic here for more details about this article) |
6/20. Florid cemento-osseous dysplasia in a young Indian woman. A case report.We present a rare case of florid cemento-osseous dysplasia (FCOD) occurring in a 27-year-old Indian woman. She presented with three lesions, two of them symmetrical, at the posterior region of the mandible. Another lesion appeared nine months later, symmetrical to the existing third lesion. This confirmed the diagnosis of florid cemento-osseous dysplasia as being symmetrical asymptomatic bone lesions occurring in the jaw. The diagnosis was made radiographically depending on a series of radiographs, as biopsy is contraindicated. No treatment was required as the lesions were asymptomatic, causing no problem to the patient. The patient continues to be reviewed annually. The case is rare in its unusual combination of the disease itself (FCOD), age (27 years) and race (Indian). Clinical and radiological features are presented.- - - - - - - - - - ranking = 1.0572333612215keywords = mandible, jaw (Clic here for more details about this article) |
7/20. Pyle's disease: an incidental finding in a routine dental patient.Pyle's disease (PD) or metaphyseal dysplasia is an extremely rare genetic disorder, transmitted as an autosomal recessive trait. The peculiarity of the disease is that the striking radiographic manifestations contrast with the relatively normal clinical features. The oral findings and radiographic features of the disease are not well documented. The present paper describes the radiographic features of Pyle's disease in a 17-year-old girl and draws attention to the findings in the jaw bones.- - - - - - - - - - ranking = 0.057233361221491keywords = jaw (Clic here for more details about this article) |
8/20. Dental findings and rehabilitation in familial osteodysplasia (Anderson type): a case report.Familial osteodysplasia is a disorder of osteogenesis with an autosomal recessive pattern of inheritance which predominantly affects facial bones. No recent case had been reported, particularly from a dental point of view since the syndrome was first described by Anderson et al (JAMA 1972;220:1687-93). A 23-year-old male with familial osteodysplasia was presented in maxillofacial and dental aspects with clinical and radiological manifestations including malocclusion, abnormal teeth alignment, impacted teeth, shape disturbances including uncompleted coronal formation, root shortening with bulbous form, high angled mandible and elongation of the corpus of mandible. Recognition of the syndromal features prior to any dental intervention is of paramount importance because of increased inclination to spontaneous mandibular fractures. Hence, no surgical intervention was performed for impacted teeth. Following the extractions of severely mobile teeth, a definitive restoration was fabricated as distal-extension removable partial dentures with conus crown telescopic system. The aesthetic and functional outcome was satisfactory for the patient. In conclusion, dentists appear to play an important role in the recognition of familial osteodysplasia, based on maxillofacial and dentoalveolar findings. awareness of the syndromal features, especially of spontaneous fractures, would detect the limitations for dental interventions and treatment planning.- - - - - - - - - - ranking = 2keywords = mandible (Clic here for more details about this article) |
9/20. osteomyelitis of the mandible in a patient with dysosteosclerosis. Report of a case.Dysosteosclerosis is a rare bone dysplasia that has radiographic, histopathologic, and clinical similarities to osteopetrosis. This article reviews the dental findings reported in patients with dysosteosclerosis and presents the first reported case of osteomyelitis of the mandible in a patient with this disease. This is also the first report that demonstrates ankylosis of impacted teeth in dysosteosclerosis.- - - - - - - - - - ranking = 5keywords = mandible (Clic here for more details about this article) |
10/20. A new lethal sclerosing bone dysplasia.A neonate is described with a lethal sclerosing bone dysplasia associated with prenatal fractures and craniofacial abnormalities including microcephaly, exophthalmos, hypoplastic nose and mid-face, small jaw and nodular hyperplasia of the gums. Parental consanguinity suggests that an autosomal recessive mutation is the likely aetiology.- - - - - - - - - - ranking = 0.057233361221491keywords = jaw (Clic here for more details about this article) |
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