11/58. Pseudo-Kaposi sarcoma with arteriovenous malformation.Pseudo-Kaposi sarcoma with vascular malformation (Stewart-Bluefarb syndrome) is an uncommon and important entity characterized by congenital arteriovenous malformation and skin lesions that may resemble Kaposi sarcoma. This is usually seen in the lower limb of young people. We report a case of this syndrome in a 17-year-old boy who had skin lesions on the right leg and foot.- - - - - - - - - - ranking = 1keywords = limb (Clic here for more details about this article) |
12/58. Congenital pelvic arteriovenous malformation: uncommon symptoms of lower limb venous hypertension.Congenital pelvic arteriovenous malformations (AVMs) are rare and their clinical behavior is quite variable. A case of congenital pelvic AVM manifesting with unusual extrapelvic symptoms of ipsilateral leg pain is described. The causes of symptoms associated with congenital pelvic AVMs are discussed.- - - - - - - - - - ranking = 4keywords = limb (Clic here for more details about this article) |
13/58. High-flow arteriovenous malformation of the lower extremity: ethanolamine oleate sclerotherapy.We report the case of a young man presenting with high-flow arteriovenous malformation (AVM), in whom percutaneous direct nidus puncture ethanolamine oleate (EO) sclerotherapy was useful in the management of the AVM. To our knowledge, this is the first report of percutaneous trans-nidus EO sclerotherapy for AVM in the extremities. Percutaneous trans-nidus sclerotherapy should be considered as an alternative choice for the management of symptomatic AVM.- - - - - - - - - - ranking = 41.667750284055keywords = extremity (Clic here for more details about this article) |
14/58. A case of ruptured aneurysm associated with spinal arteriovenous malformation presenting with hematomyelia: case report.BACKGROUND: spinal cord arteriovenous malformation (AVM) associated with spinal aneurysm is not particularly rare, but cases presenting with hematomyelia are relatively rare compared to those with subarachnoid hemorrhage (SAH). We report a rare case of successfully treated spinal AVM associated with ruptured aneurysm presenting with hematomyelia. CASE DESCRIPTION: A 52-year-old male was admitted to our hospital with sudden onset of tetraplegia, respiratory disturbance, and superficial sensory disturbance. Computed tomography revealed hematomyelia at the level of C3-4. gadolinium-enhanced magnetic resonance imaging showed small, enhanced lesions. angiography revealed an intradural perimedullary arteriovenous malformation associated with two aneurysms on the feeding arteries. Administration of high-dose methylprednisolone gradually ameliorated his symptoms. Direct surgical obliteration was performed on the 30th day after the onset. The bilateral C3 cervical radicular arteries and the nidus were coagulated. angiography performed after surgery showed neither the aneurysms nor the nidus. He was discharged with only mild weakness in the left upper extremity and mild left hypesthesia 3 months after surgery, and was fully independent. CONCLUSION: We report a case of hematomyelia caused by ruptured aneurysm associated with spinal arteriovenous malformation that was successfully treated with surgical obliteration.- - - - - - - - - - ranking = 10.416937571014keywords = extremity (Clic here for more details about this article) |
15/58. Extradural thoracic arteriovenous malformation in a patient with klippel-trenaunay-weber syndrome: case report.OBJECTIVE AND IMPORTANCE: spinal cord involvement in Klippel-Trenaunay-Weber (KTW) syndrome is rare. Cases of intradural spinal cord arteriovenous malformations (AVMs) have been associated with this syndrome. Likewise, cases of epidural hemangioma and angiomyolipoma have been reported to occur at the same segmental level as cutaneous hemangioma in KTW syndrome. This report details a rare case of an extradural thoracic AVM in a patient with KTW syndrome. CLINICAL PRESENTATION: A 30-year-old man presented with a 10-month history of progressive myelopathy, bilateral lower-extremity weakness, and numbness, with the right side affected more than the left. His symptoms had progressed to the point that he was unable to walk. The patient had the characteristic manifestations of KTW syndrome, including numerous cutaneous angiomas and cavernomas, limb hypertrophy and syndactyly, and limb venous malformations. A magnetic resonance imaging scan and subsequent angiogram demonstrated a large extradural AVM causing cord compression at the T3-T4 levels. INTERVENTION: The patient underwent two separate endovascular procedures, including embolization of upper thoracic and thyrocervical trunk feeders. Subsequently, he underwent T1-T4 laminectomy and microsurgical excision of the AVM. Clinically, the patient improved such that he could walk without assistance. CONCLUSION: KTW syndrome represents a spectrum of clinical presentations. Although involvement of the spinal cord is uncommon, the manifestations of this syndrome may include both intradural and extradural AVMs in addition to various tumors.- - - - - - - - - - ranking = 12.416937571014keywords = extremity, limb (Clic here for more details about this article) |
16/58. Intra-rachidian disorders: two unusual cases of recurrent abdominal pain in children.Recurrent abdominal pain (RAP) is generally thought to be of psychological origin but organic aetiologies are increasingly being identified. The cases of two children with vertebral disorders revealed by recurrent abdominal pain are reported. A 14-y-old girl presented with RAP associated with scoliosis, due to a T8-T9 intra-dural extra-medullary tumour. A 7-y-old girl who suffered from nocturnal RAP located in the right iliac fossa for 1 y had decreased muscular strength, pyramidal signs, and a 10 degree Lassegue sign in the right lower limb, revealing a vascular malformation extending from T12 to L2. Conclusion: Atypical pain and associated neurological signs or scoliosis must raise the possibility of intra-rachidian disorders. Magnetic resonance examination will then precisely state the location and nature of the pathological process, avoiding excessive delay in therapeutic management.- - - - - - - - - - ranking = 1keywords = limb (Clic here for more details about this article) |
17/58. proteus syndrome.A 34-year-old male patient was referred with a recalcitrant leg ulcer overlying an extensive vascular malformation, which had led several times to septic soft tissue infections. During his infancy he had been diagnosed to have Klippel-Trenaunay syndrome. Clinical examination revealed asymmetric hypertrophy of the lower extremities, an extensive portwine stain on the more severely affected left limb as well as prominent venous varicosities of both legs. Hands and feet showed striking cerebriform palmoplantar hypertrophy, and macrodactily with syndactily of several fingers. All toes had been amputated in early childhood due to extreme overgrowth and currently the patient walked on his forefeet in a prominent pes equinus deformity. Further symptoms consisted in several lipomas at both arms, another portwine stain at the left hemithorax and a single cafe-au-lait spot at the left scapula. Angio-magnetic resonance imaging scans of both legs showed an extensive venous-lymphatic vascular malformation involving the whole subcutis and infiltrating the muscle. The chronic wound was interpreted as venous stasis ulceration. Local percutaneous sclerotherapy of the dilated veins underneath the ulcer was discussed, but considered to carry a relevant risk of skin necrosis with consecutive progression of the wound. A conventional split-skin graft led to complete wound healing. Since, the patient consequently wears custom-made compression stockings and remained free from recurrences. The syndromatic constellation of palmoplantar overgrowth, multiple lipomas, giant fingers and toes, limb overgrowth, venous-lymphatic malformation and a cafe-au-lait spot led to the diagnosis of proteus syndrome. The possible aetiology, clinical manifestations, differential diagnosis and management of this rare disorder are discussed.- - - - - - - - - - ranking = 2keywords = limb (Clic here for more details about this article) |
18/58. spinal cord arteriovenous malformation in a person with congenital lymphatic abnormalities.spinal cord arteriovenous malformations have been described in association with a variety of congenital diseases affecting the vasculature, including klippel-trenaunay-weber syndrome, Rendu-Osler-Weber syndrome and others, but rarely in association with lymphatic abnormalities. We report the case of a young man with congenital lymphedema and arteriovenous malformations of one lower extremity and a spinal cord arteriovenous malformation. awareness of the possible presence of a central nervous system arteriovenous malformation in individuals with pre-existing arteriovenous and lymphatic abnormalities may be helpful in their diagnosis and management.- - - - - - - - - - ranking = 10.416937571014keywords = extremity (Clic here for more details about this article) |
19/58. Arteriovenous malformation of the foot: a case presentation.arteriovenous malformations have been reported as rare clinical entities in the foot. When these lesions present, they are most often found in the brain, lungs, and pelvis/thigh of the lower extremity and develop as a result of failed fetal vascular development. arteriovenous malformations can present with a variety of dermatologic and osseous manifestations. A delayed or missed diagnosis can have severe effects, including chronic ulcerations and osseous manifestations, and lead to amputation. Once identified, a complete evaluation is needed to provide the clinician with a full understanding of the magnitude of the deformity and the potential implications to the limb's vascular status after treatment. A concise review of the literature is provided with a case presentation of an arteriovenous malformation within the foot that was not suspected based on the clinical and imaging evaluation.- - - - - - - - - - ranking = 11.416937571014keywords = extremity, limb (Clic here for more details about this article) |
20/58. Surgical treatment of major vascular malformations localized to the flexor digitorum superficialis muscle: report of 3 cases.Three cases of congenital arteriovenous malformations localized to the flexor digitorum superficialis presented to a single surgeon. In all three cases, the tumours were resectable with negligible morbidity to the upper extremity.- - - - - - - - - - ranking = 10.416937571014keywords = extremity (Clic here for more details about this article) |
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